Aggressive Angiomyxoma Of The External Ear In Children: An Extremely Rare Case


  •   Houda Mounji

  •   Mohamed Elbouderkaoui

  •   Malika Benfdil

  •   Youssef Rochdi

  •   Hassan Nouri

  •   Abdelaziz Raji


Aggressive angiomyxoma is a mesenchymal tumor arising from connective tissues with a predilection to the female pelvic soft parts. Cervico-facial localization remains rare .We report here the first case of aggressive angiomyxoma of the external ear of a 7 year old patient, which was treated successfully by surgical excision. The clinical and pathologic features and radiological aspects of this tumor are discussed.

Keywords: Agressive, angiomyxoma, external ear, children


Behranwala K A, Thomas JM. Agressive angiomyxoma : a distinct clinical entity. EJOS 2003 ; 29 :559-563.

Chen YK, Lin LM, Lin CC, et al: Myxoid tumor of the oral cavity with features of superficial angiomyxoma: Report of a case. J Oral Maxillofac Surg 56:379, 1998.

Steeper TA, Rosai J. Aggressive angiomyxoma of the female pelvis and perineum. Report of nine cases of a distinctive type of gynecologic soft-tissue neoplasm. Am J Surg Pathol 1983;7:463–75.

Tavassoli, FA.; Devilee, P., editors. World Health Organization Classification of Tumours: Pathology and Genetics of Tumours of the Breast and Female Genital Organs. IARC Press; Lyon: 2003. p. 305-329.

Papachristou DJ, Batistatou A, Paraskevaidis E, Agnantis NJ. Aggressive angiomyxoma of the vagina: a case report and review of the literature. Eur J Gynaecol Oncol 2004;25:519–21

Yamashita Y, Tokunaga O, Goto M. Agressive Angiomyxoma of the Oral Floor : Report of a case. J Oral Maxillofac Surg 2004 ;62 :1429-1431.

Dufau J P, Soulard R, Verine J, Liard O, Gros P. Une lésion récidivante de la lèvre A recurrent lesion of the lip. Ann Pathol 2002 ;22 :339-40.

N. J. Rawlinson, W. West, Nelson M, and Julia A. Bridge. Aggressive Angiomyxoma with t(12;21) and HMGA2 Rearrangement: Report of a Case and Review of the Literature. Cancer Genet Cytogenet. 2008 March ; 181(2): 119–124.

Jeyadevan NN, Sohaib SA, Thomas JM, Jeyarajah A, Shepherd JH, Fisher C. Imaging features of aggressive angiomyxoma. Clin Radiol. 2003; 58(2):157–162. 15.

Outwater EK, Marchetto BE, Wagner BJ, Siegelman ES. Aggressive angiomyxoma: findings on CT and MR imaging. AJR Am J Roentgenol. 1999; 172(2):435–438.

Haldar K, Martinek IE, Kehoe S. Aggressive angiomyxoma: a case series and literature review. Eur J Surg Oncol. 2010;36(4):335–339.

Chan YM, Hon E, Ngai SW, Ng TY, Wong LC. Aggressive angiomyxoma in females: is radical resection the only option? Acta Obstet Gynecol Scand. 2000; 79(3):216–220.

Suleiman M, Duc C, Ritz S, Bieri S. Pelvic excision of large aggressive angiomyxoma in a woman: irradiation for recurrent disease. Int J Gynecol Cancer. 2006;16(suppl 1):356–360.

Begin LR, Clement PB, Kirk ME, Jothy S, McCaughey WT, Ferenczy A. Aggressive angiomyxoma of pelvic soft parts: A clinicopathologic study of nine cases. Hum Pathol 1985;16:621–628.

Siassi RM, Papadopoulos T, Matzel K. Metastasizing aggressive angiomyxoma. Engl J Med 1999;2:1772.

Blandamura S, Cruz J, Faure Vergara L, Machado Puerto I, Ninfo V. Aggressive angiomyxoma: a second case of metastasis with patient’s death. Hum Pathol 2003;34:1072–4.


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How to Cite
Mounji, H., Elbouderkaoui, M., Benfdil, M., Rochdi, Y., Nouri, H., & Raji, A. (2020). Aggressive Angiomyxoma Of The External Ear In Children: An Extremely Rare Case. European Journal of Medical and Health Sciences, 2(3).